Congenital Oval Window Aplasia: An Unusual Cause of Conductive Hearing Loss in an Adult
نویسنده
چکیده
Results: Audiometric evaluation showed a maximal unilateral left conductive hearing loss. High resolution temporal bone CT showed absence of the oval window on the left along with facial and stapes abnormalities. Exploratory tympanotomy showed an aberrant facial nerve, monopodal and abnormally located stapes and absent oval window. Postoperative hearing gain achieved after a neo-oval window and Schuknecht piston wire prosthesis remained stable over two years.
منابع مشابه
Congenital absence of the oval window: radiologic diagnosis and associated anomalies.
BACKGROUND AND PURPOSE In most children with conductive hearing loss, acquired otitis media and/or middle ear effusion are ultimately diagnosed. Congenital conductive hearing loss is a rare condition; absence of the oval window is an unusual pathogenesis for this type of hearing impairment and can be associated with an anomalous horizontal facial nerve canal. Our goal was to describe the imagin...
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INTRODUCTION Conductive hearing loss, in the presence of a normal external ear, is usually due to an interference with the normal transmission of sound from the tympanic membrane across the ossicular chain to the oval window. If conductive hearing loss occurs in a young child, congenital middle ear pathology is the most likely cause. MATERIALS AND METHODS High resolution computed tomography o...
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BACKGROUND AND PURPOSE Congenital causes of hearing loss in children commonly are encountered, and imaging aids in diagnosis as well as presurgical evaluation. Atresia of the oval window not associated with atresia of the external auditory canal (EAC) is a rare cause of congenital hearing loss in children. We present the clinical and imaging findings in children with isolated oval-window atresi...
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The occurrence of oval window atresia is a rare anomaly with conductive hearing loss. Traditional atresia surgeries involve challenging surgical techniques with risks of irreversible inner ear damage. Recent reports on Bonebridge (Medel, Innsbruck, Austria), a novel implantable bone conduction hearing aid system, assert that the device is safe and effective for conductive hearing loss. We prese...
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OBJECTIVE To present the results of our experience with labyrinthotomy or vestibulotomy in cases where the oval window is blocked by the facial nerve and in the presence of bilateral congenital agenesis of the oval window, respectively. STUDY DESIGN Retrospective analysis of the records of the patients operated in two different centers. METHODS Between 2007 and 2012, 5 ears of 4 patients wh...
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تاریخ انتشار 2016